| Catalog Number | GTX105504 |
| Product Name | NAGLU antibody |
| Full Name | N-acetylglucosaminidase, alpha- |
| Product Description | Rabbit polyclonal antibody to NAGLU (N-acetylglucosaminidase, alpha-) |
| Synonyms | MPS-IIIB | MPS3B | NAG | UFHSD |
| Background | This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq] |
| Clonality | Polyclonal |
| Host | Rabbit |
| Immunogen | Recombinant protein fragment contain a sequence corresponding to a region within amino acids 101 and 528 of NAGLU |
| Antigen Species | Human |
| Tested Applications | WB and IF. The usefulness of this product in other applications has not been determined. |
| Application Note | Suggested starting dilutions are as follows. WB: 1:500-1:3000，IF:1:100-1:200. Not yet tested in other applications. Optimal working dilutions should be determined experimentally by the end user. |
| Specificity | This antibody is specific to the Human NAGLU protein. |
| Species Cross Reactivity | Human - Not yet tested in other species |
| Positive Controls | 293T | A431 | H1299 | HeLaS3 | HepG2 | Molt-4 | Raji |
| Target | NAGLU |
| Predicted Target Size(KDa) | 82.28 |
| Form Supplied | Liquid |
| Concentration | 1 mg/ml |
| Purification | Purified by antigen-affinity chromatography. |
| Storage Buffer | 0.1M Tris, 0.1M Glycine, 10% Glycerol (pH7). 0.01% Thimerosal was added as a preservative. |
| Storage Instruction | Keep as concentrated solution. Aliquot and store at -20ºC or below. Avoid multiple freeze-thaw cycles. |
| Notes | For In vitro laboratory use only. Not for any clinical, therapeutic, or diagnostic use in humans or animals. Not for animal or human consumption. |
Image:GTX105504 WB ImageSample(30 ug whole cell lysate)A:H1299B:HeLa S3(GTX14654)C:Hep G2 (GTX27900)7.5% SDS PAGEGTX105504 diluted at 1:1000GTX105504 IF ImageImmunofluorescence analysis of HeLa, using NAGLU(GTX105504) antibody at 1:200 dilution.Print:Print
